Malignant peripheral nerve sheet tumour
Clinical features Fig 33a – Malignant peripheral nerve sheath tumor –Cohesive tissue fragment showing an epithelioid-like pattern area (H&E) Immunocytochemistry Electron microscopy Genetic studies Differential Diagnosis Main points
Neurofibroma
Clinical features Cytopathology Immunocytochemistry Differential Diagnosis Main points
Synovial sarcoma
For more details see biphasic tumour
Fibrosarcoma of infancy
Clinical features Cytopathology Genetic studies Differential Diagnosis Main points Treatment: complete excision
Fibromatosis colli
Clinical features Fig 31a – Fibromatosis colli – Single fibroblasts, and regenerating multinucleated muscle fibres (H&E) Immunocytochemistry Differential Diagnosis Main points
Fibromatosis
The term fibromatosis was proposed by Stout for a group of related conditions having in common the following features: There are three variants of fibromatosis, apparently restricted to childhoods that present distinct clinicopathological picture: fibromatosis colli, infantile digital fibromatosis and infantile myofibromatosis (for details see Soft tissue Chapter)
Nodular fasceiitis
Clinical features Fig 29 – Nodular fasciitis- Myxoid spindle cell lesion Immunocytochemistry Genetic studies Differential Diagnosis Main points
SPINDLE CELL LESIONS
Extraskeletal myxoid chondrosarcoma
Clinical features Fig 26 – Extraskeletal myxoid chondrosarcoma – Single cells or cells in small isolated groups or matrix embedded aggregates. Long delicate spicules of this matrix, with sharply defined edges, blend with the myxoid background (H&E). Histochemical Stains Immunocytochemistry Electron microscopy Genetic studies Differential Diagnosis Main points
Myxoid liposarcoma
Clinical features Fig 22 – Myxoid liposarcoma –Myxoid stroma with plexiform capillary network (Giemsa) Histochemical Stains Immunocytochemistry Genetic Studies Differential Diagnosis Main points